We present a case of an eleven-year-old boy presenting with progressive extrapyramidal signs and dementia.His imaging findings demonstrated the classic Rx - Antifungals eye-of-the-tiger sign on T2W magnetic resonance imaging.He was diagnosed with pantothenate kinase-associated neurodegeneration (PKAN).This is a rare autosomal recessive inborn error of coenzyme A metabolism, Measuring Cup caused by mutations in PANK2.
This is the first reported case of PKAN from the Caribbean.